gms | German Medical Science

65th Annual Meeting of the German Society of Neurosurgery (DGNC)

German Society of Neurosurgery (DGNC)

11 - 14 May 2014, Dresden

Atypical localization of grossly calcified Dysembryoplastic Neuroepithelial Tumor (DNET)

Meeting Abstract

  • Hakan Erdogan - Maltepe University School of Medicine, Department of Neurosurgery, Istanbul, Turkey
  • Bilal Kelten - Maltepe University School of Medicine, Department of Neurosurgery, Istanbul, Turkey
  • Seyho Cem Yucetas - Kafkas University School of Medicine, Department of Neurosurgery, Istanbul, Turkey
  • Veysel Antar - İstanbul Research and Training Hospital, Department of Neurosurgery, Istanbul, Turkey
  • Erol Tasdemiroglu - Institute of Neurological Sciences, Gelisim University, Istanbul, Turkey, Istanbul, Turkey

Deutsche Gesellschaft für Neurochirurgie. 65. Jahrestagung der Deutschen Gesellschaft für Neurochirurgie (DGNC). Dresden, 11.-14.05.2014. Düsseldorf: German Medical Science GMS Publishing House; 2014. DocP 036

doi: 10.3205/14dgnc431, urn:nbn:de:0183-14dgnc4313

Published: May 13, 2014

© 2014 Erdogan et al.
This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by-nc-nd/3.0/deed.en). You are free: to Share – to copy, distribute and transmit the work, provided the original author and source are credited.


Outline

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Objective: To report our experience with the case of grossly calcified Dysembryoplastic Neuroepithelial Tumor in Cerebellum (DNET)

Method: In our study we report a case of a 31-year-old male with headache and ataxia during the last six months. His neurological examination revealed no deficit. Magnetic resonance imaging with contrast enhancement showed well demarcated, heterogenously enhanced and disseminated signal void areas resembling hemorrhage with 35x45x56 mm dimensions of right cerebellar mass partially compressing to the brain stem. He underwent to limited craniectomy of posterior fossa and total removal of the tumor was accomplished by piece meal fashion. His postoperative period was uneventful and he was discharged from hospital on 10th day postoperatively. Histological examination showed small glial cells, oligodendrocytes-like, lying in an eosinophilic alveolar matrix with some floating neurons and extensive areas of calcification. His pathological report was Dysembryoplastic Neuroepithelial Tumor.

Results: Here we report an unusual case demonstrating that DNET may present as a totally calcified tumor of infratentorial localization.

Conclusions: DNET is a benign neoplasm of supratentorial region typically. Our case has unique findings because of the location and gross calcification of the tumor. Only four cases of cerebellar DNET and a few cases of DNETs that present gross calcification have been reported in the literature. To our knowledge, both findings in the same tumor have not been reported so far.