Artikel
Chest deformity in patients with Marfanoid habitus : clinical and anthropometrical evaluation
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Autoren
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S. Baran
- University in Zielona Gora, Department of Physical Education, Zielona Gora, Poland
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A. Ignys
- University of Medical Sciences, Poznan, Poland
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M. Glowacki
- University of Medical Sciences, Poznan, Poland
| Veröffentlicht: | 19. Oktober 2004 |
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Gliederung
Text
Introduction
Marfan syndrome, disorder of the fibrous connective tissue, inherited in an autosomal dominant way is characterised by pleiotropism and striking clinical variability. Skeletal deformities such as dolichocephaly, dolichostenomely, scoliosis and chest deformities are the basic features of Marfanoid habitus. The aim of the paper was to evaluate the structure and type of chest deformity in patients with Marfanoid habitus.
Methods
The study encompassed 55 patients (24 male and 31 female) ranging in age from 2 to 53 years. Both clinical examination and anthropometrical measurements including circumference, fibular and transversal dimensions of the chest were performed in each case. The index of chest flattening, as well as the occurrence of chest deformities were evaluated.
Results
Chest deformities were observed in 42% of patients with Marfanoid habitus, predominantly among the males. Pectus excavatum was stated in 24% and carinatum in 15% of patients. Smaller chest circumference, transversal and fibular dimensions of the chest were observed in patients with Marfanoid habitus, when compared with the general population.
Conclusions
The presented evaluation of chest deformities, underlines the need for holistic treatment of patients with Marfanoid habitus, for whom dysmorphophobia is as important a health issue as pathology within other systems of the body.
