gms | German Medical Science

68. Jahrestagung der Deutschen Gesellschaft für Unfallchirurgie
90. Tagung der Deutschen Gesellschaft für Orthopädie und Orthopädische Chirurgie
45. Tagung des Berufsverbandes der Fachärzte für Orthopädie in Zusammenarbeit mit dem Deutschen Verband für Physiotherapie – Zentralverband der Physiotherapeuten/Krankengymnasten

19. bis 23.10.2004, Berlin

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Chest deformity in patients with Marfanoid habitus : clinical and anthropometrical evaluation

Meeting Abstract (DGOOC 2004)

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  • S. Baran - University in Zielona Gora, Department of Physical Education, Zielona Gora, Poland
  • A. Ignys - University of Medical Sciences, Poznan, Poland
  • M. Glowacki - University of Medical Sciences, Poznan, Poland

Deutsche Gesellschaft für Unfallchirurgie. Deutsche Gesellschaft für Orthopädie und orthopädische Chirurgie. Berufsverband der Fachärzte für Orthopädie. 68. Jahrestagung der Deutschen Gesellschaft für Unfallchirurgie, 90. Tagung der Deutschen Gesellschaft für Orthopädie und Orthopädische Chirurgie und 45. Tagung des Berufsverbandes der Fachärzte für Orthopädie. Berlin, 19.-23.10.2004. Düsseldorf, Köln: German Medical Science; 2004. Doc04dguE8-1254

The electronic version of this article is the complete one and can be found online at: http://www.egms.de/en/meetings/dgu2004/04dgu0251.shtml

Published: October 19, 2004

© 2004 Baran et al.
This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by-nc-nd/3.0/deed.en). You are free: to Share – to copy, distribute and transmit the work, provided the original author and source are credited.

Outline

Text

Introduction

Marfan syndrome, disorder of the fibrous connective tissue, inherited in an autosomal dominant way is characterised by pleiotropism and striking clinical variability. Skeletal deformities such as dolichocephaly, dolichostenomely, scoliosis and chest deformities are the basic features of Marfanoid habitus. The aim of the paper was to evaluate the structure and type of chest deformity in patients with Marfanoid habitus.

Methods

The study encompassed 55 patients (24 male and 31 female) ranging in age from 2 to 53 years. Both clinical examination and anthropometrical measurements including circumference, fibular and transversal dimensions of the chest were performed in each case. The index of chest flattening, as well as the occurrence of chest deformities were evaluated.

Results

Chest deformities were observed in 42% of patients with Marfanoid habitus, predominantly among the males. Pectus excavatum was stated in 24% and carinatum in 15% of patients. Smaller chest circumference, transversal and fibular dimensions of the chest were observed in patients with Marfanoid habitus, when compared with the general population.

Conclusions

The presented evaluation of chest deformities, underlines the need for holistic treatment of patients with Marfanoid habitus, for whom dysmorphophobia is as important a health issue as pathology within other systems of the body.