Article
Pierre Robin Syndrome in Otorhinolaryngology
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Authors
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Irén Csiszér
- "Iuliu Haţieganu" University of Medicine and Pharmacy Cluj-Napoca, Galenus Medi, Singeorgiu de Mures, Romania
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Neagos Adriana
- Galenus Medical Center, Tirgu Mures,, Romania
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Florea Constantin
- Galenus Medical Center, Tirgu Mures,, Romania
| Published: | April 13, 2017 |
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Outline
Text
Introduction: Pierre Robin syndrome (PRS) is a rare congenital condition of facial abnormalities. The three main characteristics are: cleft palate, retrognathia and glossoptosis.
Methods: We present the case study of a new born baby with PRS. At birth the baby had following anatomical modification: micrognathia, microstomy, severe retrognathia, microglossia and complete posterior cleft palate. Immediatly after birth she presented severe respiratory and feeding difficulty for which, in 24 hours after birth we performed a tracheostomy and we placed a nasogastric feeding tube. Cardiovascular findings such as benign murmurs, patent ductus arteriosus, patent foramen ovale, atrial and ventricular septal defect have all been documented.
Results: We will discuss about the complications and treatments of the PRS, that appeared until the age of three.
Conclusion: The tracheostomy in severe PRS cases is vital, but it is not enough to ensure a complete rehabilitation of the patient. In order to achieve good results, the issue must be approached in a multidisciplinary mode that includes: otorhinolaryngologist, psychologist, plastic or maxillofacial surgeon, orthodontist and speech or language therapist.
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