Artikel
Esophageal lung with congenital tracheal stenosis: an extremely rare variant of communicating bronchopulmonary foregut malformation
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Autoren
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Michael Berger
- Dr. von Haunersches Kinderspital, Kinderchirurgische Klinik, München
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José Antonio Matute de Cárdenas
- Hospital Universitario Virgen de Rocío, Thoracic and Airway Surgery Unit, Department of Pediatric Surgery, Sevilla
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Alejandro Adsuar Gomez
- Hospital Universitario Virgen de Rocío, Department of Cardiac Surgery, Seville
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Juan Carlos de Agustín Asencio
- Hospital Universitario Virgen de Rocío, Thoracic and Airway Surgery Unit, Department of Pediatric Surgery, Sevilla
| Veröffentlicht: | 26. April 2013 |
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Gliederung
Text
Introduction: Esophageal lung is a rare variant of communicating bronchopulmonary foregut malformation that can be associated with esophageal atresia. Ten cases are reported so far. Treatment options are detachment with complete pulmonary resection versus detachment and reinsertion into the trachea.
Material and methods: Here we present jet another child with such a rare variant.
Results: The right main bronchus originated from an otherwise healthy esophagus and was associated with congenital tracheal stenosis. The child underwent reinsertion of the bronchus at the level of the carina and simultaneous slide tracheoplasty under cardiopulmonary bypass support. Unfortunately, the child died from a bronchopleural fistula with massive airleak during the postoperative course.
Conclusion: To our best knownledge, this was the first time a one stage approach was intented for this particular malformation. We describe the clinical presentation, diagnostic workup and management possibilities for this extremely rare variant of foregut malformations.
