Artikel
Surgical management of neonatal respiratory distress caused by giant extra-laryngeal vascular malformations
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Veröffentlicht: | 4. April 2012 |
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Gliederung
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The most common vascular malformation causing respiratory distress in neonates is intralaryngeal hemangioma. The authors report rare cases of huge extralaryngeal vascular lesions which caused severe upper airway obstruction requiring intubation right after delivery (CHAOS syndrome). Case 1 is a congenital lympho-venous hamartoma originating from the submandibular gland and involving the lower face, the cervical, supraclavicular and jugular region, the floor of the mouth, and the upper mediastinum. Case 2 is a giant congenital hemangiopericytoma arising from the base of tongue. Preoperative radiological examination was in favor of possible hemangioma in both cases. The airway could be assured by radical excision of the mass from external approach without tracheotomy. Follow-up radiological examinations showed no recurrence within 3 and 1 years after surgery, respectively. However nowadays therapy of vascular lesions is focused on conservative treatment (e.g. systemic propranolol), our cases demonstrate the necessity of histological confirmation and prompt and strict radical excision of malformations in special conditions.