gms | German Medical Science

83. Jahresversammlung der Deutschen Gesellschaft für Hals-Nasen-Ohren-Heilkunde, Kopf- und Hals-Chirurgie e. V.

Deutsche Gesellschaft für Hals-Nasen-Ohren-Heilkunde, Kopf- und Hals-Chirurgie e. V.

16.05. - 20.05.2012, Mainz

Surgical management of neonatal respiratory distress caused by giant extra-laryngeal vascular malformations

Meeting Abstract

  • corresponding author Adam Perenyi - Dept. of Otorhinolaryngology, Head and Neck Surgery, Szeged, Hungary
  • Katalin Bartyik - Department of Pediatrics, University of Szeged, Szeged, Hungary
  • Laszlo Tiszlavicz - Department of Pathology, Unversity of Szeged, Szeged, Hungary
  • Laszlo Rovo - Dept. of Otorhinolaryngology, Szeged, Hungary
  • Balazs Sztano - Dept. of Otorhinolaryngology, University of Szeged, Szeged, Hungary
  • Gabriella Kecskes - Dept. of Otorhinolaryngology, University of Szeged, Szeged, Hungary

Deutsche Gesellschaft für Hals-Nasen-Ohren-Heilkunde, Kopf- und Hals-Chirurgie. 83. Jahresversammlung der Deutschen Gesellschaft für Hals-Nasen-Ohren-Heilkunde, Kopf- und Hals-Chirurgie. Mainz, 16.-20.05.2012. Düsseldorf: German Medical Science GMS Publishing House; 2012. Doc12hnod169

doi: 10.3205/12hnod169, urn:nbn:de:0183-12hnod1694

Veröffentlicht: 4. April 2012

© 2012 Perenyi et al.
Dieser Artikel ist ein Open Access-Artikel und steht unter den Creative Commons Lizenzbedingungen (http://creativecommons.org/licenses/by-nc-nd/3.0/deed.de). Er darf vervielf&aauml;ltigt, verbreitet und &oauml;ffentlich zug&aauml;nglich gemacht werden, vorausgesetzt dass Autor und Quelle genannt werden.


Gliederung

Text

The most common vascular malformation causing respiratory distress in neonates is intralaryngeal hemangioma. The authors report rare cases of huge extralaryngeal vascular lesions which caused severe upper airway obstruction requiring intubation right after delivery (CHAOS syndrome). Case 1 is a congenital lympho-venous hamartoma originating from the submandibular gland and involving the lower face, the cervical, supraclavicular and jugular region, the floor of the mouth, and the upper mediastinum. Case 2 is a giant congenital hemangiopericytoma arising from the base of tongue. Preoperative radiological examination was in favor of possible hemangioma in both cases. The airway could be assured by radical excision of the mass from external approach without tracheotomy. Follow-up radiological examinations showed no recurrence within 3 and 1 years after surgery, respectively. However nowadays therapy of vascular lesions is focused on conservative treatment (e.g. systemic propranolol), our cases demonstrate the necessity of histological confirmation and prompt and strict radical excision of malformations in special conditions.