gms | German Medical Science

Fourth International Symposium and Workshops: Objective Measures in Cochlear Implants

Medical University of Hannover

01.06. bis 04.06.2005, Hannover

Neurophysiologic results in infants with auditory neuropathy/dys-synchrony related to cochlear implant candidacy

Meeting Abstract

  • corresponding author P. Kileny - University of Michigan Medical School
  • B.M. Edwards - University of Michigan Medical School
  • L.A. Van Riper - University of Michigan Medical School
  • M.B. O'Sullivan - University of Michigan Medical School
  • T.A. Zwolan - University of Michigan Medical School

Medical University of Hannover, Department of Otolaryngology. Fourth International Symposium and Workshops: Objective Measures in Cochlear Implants. Hannover, 01.-04.06.2005. Düsseldorf, Köln: German Medical Science; 2005. Doc05omci040

The electronic version of this article is the complete one and can be found online at: http://www.egms.de/en/meetings/omci2005/05omci040.shtml

Published: May 31, 2005

© 2005 Kileny et al.
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Outline

Text

Patients with auditory neuropathy (AN) present with significant sensorineural hearing loss, poor speech perception and impaired temporal processing. The diagnosis is based on discrepancies between different objective measures: cochlear microphonics and otoacoustic emissions are present indicating unimpaired outer hair cell function, the auditory brainstem response and the cochlear nerve action potential are absent. There have been reports on children with a diagnosis of AN who have benefited from cochlear implantation, as well as reports of hearing recovery in patients with a diagnosis of AN. This presentation demonstrates that similar initial clinical result patterns may have different final outcomes: in particular, when associated with hyperbilirubinemia, the "typical" AN test results may be reversible. In other cases, they persist and the patient is a cochlear implant candidate. We will also demonstrate the value of the perioperative, transtympanic, electrically-evoked ABR in AN patients.