Figure 1
Colour fundus photographs (top row): overall increased translucence of the RPE with visible choroidal vasculature. Area of atrophy in the inferior macula of the right eye is more extensive than in the left eye, where the location is nasal. Also, in the right eye the atrophy is closer to the foveola as compared with the left side. Very few microaneurysms/dot haemorrhages in the macula of both eyes, better visible under magnification (bottom right, arrows).
Blue light autofulorescence image (bottom row; right eye: composite of 2 images of the macula and optic disc) clearly shows the extent of the retinal atrophy and reveals the true extent of the retinal pathology with characteristic “salt and pepper” mottled hyper- and hypoautofluoresence beyond vascular arcades and in nasal peripapillary area.