gms | German Medical Science

62nd Annual Meeting of the German Society of Neurosurgery (DGNC)
Joint Meeting with the Polish Society of Neurosurgeons (PNCH)

German Society of Neurosurgery (DGNC)

7 - 11 May 2011, Hamburg

Extracranial-intracranial bypass surgery followed by endovascular carotid artery occlusion as a multimodal concept to treat a giant internal carotid artery aneurysm in a patient suffering from Ehlers-Danlos disease: A case report

Meeting Abstract

  • J. Perrin - Neurochirurgische Klinik, Heinrich-Heine-Universität, Düsseldorf
  • B. Turowski - Institut für Radiologie, Heinrich-Heine-Universität, Düsseldorf
  • H.J. Steiger - Neurochirurgische Klinik, Heinrich-Heine-Universität, Düsseldorf
  • D. Hänggi - Neurochirurgische Klinik, Heinrich-Heine-Universität, Düsseldorf

Deutsche Gesellschaft für Neurochirurgie. Polnische Gesellschaft für Neurochirurgen. 62. Jahrestagung der Deutschen Gesellschaft für Neurochirurgie (DGNC), Joint Meeting mit der Polnischen Gesellschaft für Neurochirurgen (PNCH). Hamburg, 07.-11.05.2011. Düsseldorf: German Medical Science GMS Publishing House; 2011. DocP 005

doi: 10.3205/11dgnc226, urn:nbn:de:0183-11dgnc2261

Published: April 28, 2011

© 2011 Perrin et al.
This is an Open Access article distributed under the terms of the Creative Commons Attribution License ( You are free: to Share – to copy, distribute and transmit the work, provided the original author and source are credited.



Objective: After reviewing literature, it was found that there is extremely little data on the surgical treatment of aneurysms in patients suffering from Ehlers-Danlos disease. The purpose of the present case-report is to present a feasible combined surgical and endovascular strategy in a patient suffering from Ehlers-Danlos disease.

Methods: In this case report we describe a successful interdisciplinary approach applied to a 42-year-old man with a continuously growing extracranial giant aneurysm of the right internal carotid artery (ICA) suffering from Ehlers-Danlos disease. An additional review of literature is provided.

Results: A 42-year-old man was admitted to our department with a continuously growing extracranial giant aneurysm of the right ICA with approximately 91.9 mm in diameter. Based on an interdisciplinary decision-making process, the first step was to perform a double-barrelled extra-intracranial bypass (STA-MCA) because the preoperative balloon occlusion test (BTO) was negative. Second the aneurysm was trapped endovascularly by coiling. The patient tolerated both interventions without any deficits; the trapped aneurysm was punctured twice to achieve a cosmetically good result. To the best of our knowledge after reviewing the literature, this is the first report on a patient suffering from a giant ICA aneurysm due to Ehlers-Danlos disease, who was treated successfully in a combined surgical and endovascular approach.

Conclusions: The present case report described a possible therapeutic strategy in a patient suffering from a giant ICA aneurysm based on Ehlers-Danlos disease, who was succesfully treated with a combined surgical and endovascular approach.