gms | German Medical Science

57th Annual Meeting of the German Society of Neurosurgery
Joint Meeting with the Japanese Neurosurgical Society

German Society of Neurosurgery (DGNC)

11 - 14 May, Essen

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Clear cell petro-clival meningioma in a 5-year old child: case report

Fallbericht eines 5-jährigen Kindes mit einem petroclivalen klarzelligen Meningeom

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  • corresponding author M. Kirsch - Neurochirurgische Klinik und Poliklinik, Carl Gustav Carus Universitätsklinikum, Technische Universität Dresden
  • P. Weigel - Neurochirurgische Klinik und Poliklinik, Carl Gustav Carus Universitätsklinikum, Technische Universität Dresden
  • G. Schackert - Neurochirurgische Klinik und Poliklinik, Carl Gustav Carus Universitätsklinikum, Technische Universität Dresden

Deutsche Gesellschaft für Neurochirurgie. Japanische Gesellschaft für Neurochirurgie. 57. Jahrestagung der Deutschen Gesellschaft für Neurochirurgie e.V. (DGNC), Joint Meeting mit der Japanischen Gesellschaft für Neurochirurgie. Essen, 11.-14.05.2006. Düsseldorf, Köln: German Medical Science; 2006. DocP 08.114

The electronic version of this article is the complete one and can be found online at: http://www.egms.de/en/meetings/dgnc2006/06dgnc331.shtml

Published: May 8, 2006

© 2006 Kirsch et al.
This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by-nc-nd/3.0/deed.en). You are free: to Share – to copy, distribute and transmit the work, provided the original author and source are credited.

Outline

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Methods: This case of a 5-year old girl that presented with a one-week history of cephalgia, ataxia and left sided torticollis. Prior to this, the girl was normally developed without any pathological signs. MR-imaging revealed a dumpbell-shaped homogenously Gadolinium-enhancing mass in the left cerebello-pontine angle and the left temporal fossa adjacent to the cavernous sinus and the major vessels of the anterior and posterior circulation. There was a massive displacement of the brainstem and mesencephalon.

Results: A staged operative approach was chosen. First, a suboccipital craniotomy was performed and the tumour was resected completely within the posterior fossa. All cranial nerves were pushed apart without a clear nerval or dural matrix. A second operation via a modified fronto-temporal craniotomy was performed three months later. Between operations, further tumour growth was observed. A complete removal of the tumour was achieved. The follow-up examinations over the past 4 years did not reveal any residual tumour or recurrence. The child recovered completely and is developing normally.

Conclusions: Clear cell meningiomas are classified as WHO °II meningiomas with an increased risk for recurrence. They represent a rare subtype that is more frequent in children. This case presents a rare tumour of extensive dimensions that is discussed with respect to molecular diagnostics.