gms | German Medical Science

77. Jahresversammlung der Deutschen Gesellschaft für Hals-Nasen-Ohren-Heilkunde, Kopf- und Hals-Chirurgie e. V.

Deutsche Gesellschaft für Hals-Nasen-Ohren-Heilkunde, Kopf- und Hals-Chirurgie e. V.

24.05. - 28.05.2006, Mannheim

Monaural deafness because of sinistral vestibulocochlear nerve abnormality

Monaurale Surditas bei N. vestibulocochlearis - Missbildung links

Meeting Abstract

  • corresponding author presenting/speaker Oliver Goldschmidt - Klinik für Phoniatrie, Pädaudiologie und Kommunikationsstörungen, Universitätsklinikum Aachen - RWTH, Aachen, Deutschland
  • author Katrin Goldschmidt - Klinik für Phoniatrie, Pädaudiologie und Kommunikationsstörungen, Universitätsklinikum Aachen - RWTH, Aachen, Deutschland
  • author Christiane Neuschaefer-Rube - Klinik für Phoniatrie, Pädaudiologie und Kommunikationsstörungen, Universitätsklinikum Aachen - RWTH, Aachen, Deutschland

German Society of Otorhinolaryngology, Head and Neck Surgery. 77th Annual Meeting of the German Society of Otorhinolaryngology, Head and Neck Surgery. Mannheim, 24.-28.05.2006. Düsseldorf, Köln: German Medical Science; 2006. Doc06hno078

Die elektronische Version dieses Artikels ist vollständig und ist verfügbar unter: http://www.egms.de/de/meetings/hno2006/06hno078.shtml

Veröffentlicht: 7. September 2006

© 2006 Goldschmidt et al.
Dieser Artikel ist ein Open Access-Artikel und steht unter den Creative Commons Lizenzbedingungen (http://creativecommons.org/licenses/by-nc-nd/3.0/deed.de). Er darf vervielf&aauml;ltigt, verbreitet und &oauml;ffentlich zug&aauml;nglich gemacht werden, vorausgesetzt dass Autor und Quelle genannt werden.


Gliederung

Text

Congenital hearing disorders can be associated with aplasia or hypoplasia of the vestibulocochlear nerve [1]. With monaural or binaural hearing disorders in children further paediatric and neurological diagnostics as well as radiological investigations are necessary apart from the paedaudiological diagnostics and treatment [2]. In addition magnet resonance tomography (MRT) and cranial computer tomography are needed in high-grade hearing disorders as preliminary investigation when e.g. Cochlea implantation is planned. The necessity for these investigations sometimes is doubted because of expenditure of time, stationary stay and sedation especially when children are disabled or have severe comorbidities. Regarding the development and paedaudiological treatment of a young boy (unilateral, sinistral deafness, see figure 1 [Fig. 1]) we want to point out that a hearing loss has to be controlled by cranial tomography. The MRT accomplished in the Department for Neuroradiology at the University Hospital Aachen (Gyroscan Intera T15) resulted in aplasia and / or hypoplasia of the sinistral nervus vestibulocochlearis. Parts of the sinister facial nerve are still recognizable in the inner acoustic meatus (see figure 2 [Fig. 2]). The meaning of tomography for adequate paedaudiologic treatment especially in congenital hearing disorders [3] is an important component of the therapy that has to be discussed with patients or adult relatives. Furthermore, technical increasingly optimized imaging results - morphologically seen - in improved diagnostic possibilities. With missing reproduction of Jewett-V-potentials in BERA-diagnostics and regarding hypo- or aplasia of the vestibulocochlear nerve in tomography - as a consequence - supply of hearing aids (including e.g. bone anchored hearing aids) with exception of the possibility of a CROS hearing aid supply is inadvisable. With contra lateral healthy and normal sense of hearing however the supply of a CROS hearing aid - particularly with children - is not always possible, since an acceptance often can not be attained by the patient and his relatives.


References

1.
Knapp FB, Klenzner T, Hamad M, Aschendorff A, Laszig R. Aplasie und Hypoplasie des N. vestibulocochlearis: Einfluss auf die Cochlear Implantation. Laryngorhinootologie 2004; 83
2.
Czerny C, Gstöttner W, Imhof H. Computertomographie und Magnetresonanztomographie kongenitaler Veränderungen des äußeren Ohrs, Mittel- und Innenohrs sowie des inneren Gehörgangs. Radiologe 2003; 43: 227–233
3.
Marangos N. Dysplasien des Innenohres und inneren Gehörganges. HNO 2002; 50: 866–881