gms | German Medical Science

57. Jahrestagung der Deutschen Gesellschaft für Neurochirurgie e. V. (DGNC)
Joint Meeting mit der Japanischen Gesellschaft für Neurochirurgie

Deutsche Gesellschaft für Neurochirurgie (DGNC) e. V.

11. bis 14.05.2006, Essen

Angiolipoma – a rare intraspinal tumour. Report of two pediatric cases

Das Angiolipom – ein seltener intraspinaler Tumor. Zwei pädiatrische Kasuistiken

Meeting Abstract

  • corresponding author R. Kahl - Klinik für Neurochirurgie, Carl-Thiem-Klinikum Cottbus
  • D. Class - Kinderneurochirurgische Abteilung, Katharinenhospital Stuttgart
  • E. Dirik - Klinik für Neurochirurgie, Katharinenhospital Stuttgart
  • J.R. Iglesias-Rozas - Institut für Pathologie, Katharinenhospital Stuttgart
  • R. Michilli - Kinderneurochirurgische Abteilung, Katharinenhospital Stuttgart

Deutsche Gesellschaft für Neurochirurgie. Japanische Gesellschaft für Neurochirurgie. 57. Jahrestagung der Deutschen Gesellschaft für Neurochirurgie e.V. (DGNC), Joint Meeting mit der Japanischen Gesellschaft für Neurochirurgie. Essen, 11.-14.05.2006. Düsseldorf, Köln: German Medical Science; 2006. DocP 08.116

Die elektronische Version dieses Artikels ist vollständig und ist verfügbar unter: http://www.egms.de/de/meetings/dgnc2006/06dgnc333.shtml

Veröffentlicht: 8. Mai 2006

© 2006 Kahl et al.
Dieser Artikel ist ein Open Access-Artikel und steht unter den Creative Commons Lizenzbedingungen (http://creativecommons.org/licenses/by-nc-nd/3.0/deed.de). Er darf vervielf&aauml;ltigt, verbreitet und &oauml;ffentlich zug&aauml;nglich gemacht werden, vorausgesetzt dass Autor und Quelle genannt werden.


Gliederung

Text

Objective: We report two cases of intraspinal angiolipoma adding to the scarce case descriptions of this entity.

Methods: A 14-year-old boy presented with a subacute paraplegia without loss of sensitivity, associated with high thoracic pain and urinary disturbances. MRI revealed an intraspinal extradural left-sided tumour at T1-3 level displacing the myelon and showing moderate contrast enhancement. On instant operation including osteoplastic laminotomy at T1-4 level a grey and massively vascularized epidural tumour with adipose tissue components was subtotally excised, demanding extensive intraoperative hemostasis. Paraplegia was completely reversible, MRI controls up to 31 months postoperatively revealed residual tumour without progression or compression of the myelon. An 11 month old boy presented with deterioration in crawling and standing, reduced spontaneous motion of the upper extremities and a constant anteflexion of the cervical spine, CSF showed increased protein content without pleocytosis. MRI disclosed an epidural space occupying process between C2 and T5 level including a separable process at T7 level with marginal contrast enhancement. A non-coagulated epidural hematoma was evacuated, at T7 level a small epidural tumour excised. The postoperative course was characterized by an epidural rebleeding necessitating evacuation and by a residual paresis of the right upper extremity.

Results: Histological evaluation in the first case demonstrated dilated vessels, primarily of venous phenotype, amongst fat tissue. In the second case the small tumour giving rise to the epidural hematoma was found to contain richly vascularized adipose tissue with siderophages, collagenous and elastic fibres.

Conclusions: The histologies correspond to spinal angiolipomas, benign tumours composed of mature adipose and abnormal vascular elements, representing a distinct rare entity and between 0.04% and 1.2% of all spinal axis tumours. The two cases reported underline the possibly acute clinical presentation of these tumours due to myeloncompression or spontaneous hemorrhage.