gms | German Medical Science

56. Jahrestagung der Deutschen Gesellschaft für Neurochirurgie e. V. (DGNC)
3èmes journées françaises de Neurochirurgie (SFNC)

Deutsche Gesellschaft für Neurochirurgie e. V.
Société Française de Neurochirurgie

07. bis 11.05.2005, Strasbourg

Bobble-head-doll syndrome associated with suprasellar cyst in children: report of three cases

Das Bobble head doll Syndrom assoziert mit der suprasellären Zyste in Kindern: Beschreibung von drei Fällen

Meeting Abstract

  • corresponding author D. Hořínek - Department of Pediatric Neurosurgery, University Hospital Motol, Prague, Czech Republic
  • M. Tichý - Department of Pediatric Neurosurgery, University Hospital Motol, Prague, Czech Republic
  • M. Jakubec - Department of Neurosurgery, University Hospital Hradec Králové, Czech Republic
  • L. Paulas - Department of Pediatric Neurology, University Hospital Motol, Prague, Czech Republic
  • M. Kyncl - Department of Radiology, University Hospital Motol, Prague, Czech Republic
  • I. Kolář - Department of Radiology, University Hospital Motol, Prague, Czech Republic

Deutsche Gesellschaft für Neurochirurgie. Société Française de Neurochirurgie. 56. Jahrestagung der Deutschen Gesellschaft für Neurochirurgie e.V. (DGNC), 3èmes journées françaises de Neurochirurgie (SFNC). Strasbourg, 07.-11.05.2005. Düsseldorf, Köln: German Medical Science; 2005. Doc10.05.-11.05

Die elektronische Version dieses Artikels ist vollständig und ist verfügbar unter: http://www.egms.de/de/meetings/dgnc2005/05dgnc0141.shtml

Veröffentlicht: 4. Mai 2005

© 2005 Hořínek et al.
Dieser Artikel ist ein Open Access-Artikel und steht unter den Creative Commons Lizenzbedingungen (http://creativecommons.org/licenses/by-nc-nd/3.0/deed.de). Er darf vervielf&aauml;ltigt, verbreitet und &oauml;ffentlich zug&aauml;nglich gemacht werden, vorausgesetzt dass Autor und Quelle genannt werden.


Gliederung

Text

Objective

We report three cases of bobble-head-doll syndrome in children with suprasellar cysts who were treated with neuroendoscopic approach.

Methods

The history and clinical features of three children (two girls and a boy, 4,2 and 9 years old) with bobble-head-doll syndrome associated with suprasellar cyst are described.

The bobble-head-doll syndrome was the initial symptom in one case. In two other cases, the macrocephaly and psychomotor retardation were the first symptoms and the bobble head-doll syndrome developed later on. The obstructive hydrocephalus was present in all three subjects.

All three children were treated with neuroendoscopic approach. The ventriculocystostomy was performed in two cases. and ventriculocystocisternostomy in one case. In one case the insertion of cystoperitoneal shunt into the ventriculocystostomy was carried out because of the recurrence of the symptoms.

Results

The abnormal head movements improved after surgery in all three children, with complete resolution of symptoms in two cases. In one case a slight nodding to-and-fro persists on walking.

Conclusions

Neuroendoscopic treatment is a procedure of first choice in symptomatic suprasellar cysts. Both ventriculocystostomy and ventriculocystocisternostomy may lead to the resolution of bobble-head-doll syndrome. According to the literature the bobble-head-doll movement relates to the compression of the dorsomedial nucleus of the thalamus.

The study has been supported by IGA grant ND/7678-3.